What is noncompaction cardiomyopathy?
Non-compaction cardiomyopathy (NCM) is a myocardial disorder, which is thought to occur due to the failure of left ventricle (LV) compaction during embryogenesis, leading to distinct morphological characteristics in the ventricular chamber.
What does non compacted mean?
Left ventricular noncompaction is a heart (cardiac) muscle disorder that occurs when the lower left chamber of the heart (left ventricle), which helps the heart pump blood, does not develop correctly. Instead of the muscle being smooth and firm, the cardiac muscle in the left ventricle is thick and appears spongy.
What is non compaction syndrome?
Noncompaction cardiomyopathy (NCC) is a rare congenital disease of heart muscle that affects both children and adults. It results from abnormal prenatal development of heart muscle. Noncompaction cardiomyopathy. Other names. Spongiform cardiomyopathy.
How is left ventricular noncompaction diagnosed?
The diagnosis of LVNC is based on cardiac testing, family history, medical history, and physical exam. Cardiac testing: An echocardiogram is the most common test used to diagnose LVNC, as the trabeculations within the left ventricle and overall squeeze of the heart can be measured with this test.
Is non compaction cardiomyopathy serious?
Left ventricular non-compaction (LVNC) is a very rare congenital cardiomyopathy. It is a disease of endomyocardial trabeculations that increase in number and prominence. This cardiomyopathy carries a high risk of malignant arrhythmias, thromboembolic phenomenon and left ventricular dysfunction.
What is the treatment for non compaction cardiomyopathy?
Medicine to treat LVNC Your doctor might prescribe certain drugs to treat LVNC. These include: Blood thinners to reduce the risk of blood clots. Beta blockers to help control heart beats and lower blood pressure.